ICD-10-CM (2010)/CHAPTER 6

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ICD-10-CM TABULAR LIST of DISEASES and INJURIES  (2010) 
CHAPTER 6 - Diseases of the nervous system (G00-G99)

Contents

Diseases of the nervous system (G00-G99)[edit]

Excludes2: certain conditions originating in the perinatal period (P04-P96)
certain infectious and parasitic diseases (A00-B99)
complications of pregnancy, childbirth and the puerperium (O00-O99)
congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
endocrine, nutritional and metabolic diseases (E00-E90)
injury, poisoning and certain other consequences of external causes (S00-T98)
neoplasms (C00-D48)
symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
This chapter contains the following blocks:
G00-G09 Inflammatory diseases of the central nervous system
G10-G14 Systemic atrophies primarily affecting the central nervous system
G20-G26 Extrapyramidal and movement disorders
G30-G32 Other degenerative diseases of the nervous system
G35-G37 Demyelinating diseases of the central nervous system
G40-G47 Episodic and paroxysmal disorders
G50-G59 Nerve, nerve root and plexus disorders
G60-G64 Polyneuropathies and other disorders of the peripheral nervous system
G70-G73 Diseases of myoneural junction and muscle
G80-G83 Cerebral palsy and other paralytic syndromes
G89-G99 Other disorders of the nervous system

Inflammatory diseases of the central nervous system (G00-G09)[edit]

G00 Bacterial meningitis, not elsewhere classified[edit]

Includes bacterial arachnoiditis
bacterial leptomeningitis
bacterial meningitis
bacterial pachymeningitis
Excludes1: bacterial:
meningoencephalitis (G04.2)
meningomyelitis (G04.2)
G00.0 Hemophilus meningitis
Meningitis due to Hemophilus influenzae
G00.1 Pneumococcal meningitis
G00.2 Streptococcal meningitis
Use additional code to further identify organism (B95.0-B95.5)
G00.3 Staphylococcal meningitis
Use additional code to further identify organism (B95.6-B95.8)
G00.8 Other bacterial meningitis
Meningitis due to Escherichia coli
Meningitis due to Friedl?nder bacillus
Meningitis due to Klebsiella
Use additional code to further identify organism (B96.-)
G00.9 Bacterial meningitis, unspecified
Meningitis due to gram-negative bacteria, unspecified
Purulent meningitis NOS
Pyogenic meningitis NOS
Suppurative meningitis NOS

G01 Meningitis in bacterial diseases classified elsewhere[edit]

Code first underlying disease
Excludes1: meningitis (in):
gonococcal (A54.81)
leptospirosis (A27.81)
listeriosis (A32.11)
Lyme disease (A69.21)
meningococcal (A39.0)
neurosyphilis (A52.13)
tuberculosis (A17.0)
meningoencephalitis and meningomyelitis in bacterial diseases classified elsewhere (G05)

G02 Meningitis in other infectious and parasitic diseases classified elsewhere[edit]

Code first underlying disease, such as:
poliovirus infection (A80.-)
Excludes1: meningitis (due to):
candidal (B37.5)
coccidioidomycosis (B38.4)
cryptococcal meningitis (B45.1)
herpesviral [herpes simplex] (B00.3)
infectious mononucleosis (B27.-2)
measles (B05.1)
mumps (B26.1)
rubella (B06.02)
varicella [chickenpox] (B01.0)
zoster (B02.1)
meningoencephalitis and meningomyelitis in other infectious and parasitic diseases classified elsewhere (G05)

G03 Meningitis due to other and unspecified causes[edit]

Includes arachnoiditis NOS
leptomeningitis NOS
meningitis NOS
pachymeningitis NOS
Excludes1: meningoencephalitis (G04.-)
meningomyelitis (G04.-)
G03.0 Nonpyogenic meningitis
Aseptic meningitis
Nonbacterial meningitis
G03.1 Chronic meningitis
G03.2 Benign recurrent meningitis [Mollaret]
G03.8 Meningitis due to other specified causes
G03.9 Meningitis, unspecified
Arachnoiditis (spinal) NOS

G04 Encephalitis, myelitis and encephalomyelitis[edit]

Includes acute ascending myelitis
meningoencephalitis
meningomyelitis
Excludes1: encephalopathy NOS (G93.40)
Excludes2: acute transverse myelitis (G37.3-)
alcoholic encephalopathy (G31.2)
benign myalgic encephalomyelitis (G93.3)
multiple sclerosis (G35)
subacute necrotizing myelitis (G37.4)
toxic encephalitis (G92)
toxic encephalopathy (G92)
G04.0 Acute disseminated encephalitis and encephalomyelitis (ADEM)
Excludes1: acute necrotizing hemorrhagic encephalopathy (G04.3-)
G04.00 Postinfectious acute disseminated encephalitis and encephalomyelitis (postinfectious ADEM)
Acute disseminated encephalitis and encephalomyelitis NOS
Excludes1: noninfectious acute disseminated encephalomyelitis (noninfectious ADEM) (G04.81)
postchickenpox encephalitis (B01.1)
postmeasles encephalitis (B05.0)
postmeasles myelitis (B05.1)
G04.01 Postimmunization acute disseminated encephalitis, myelitis and encephalomyelitis
Encephalitis, postimmunization
Encephalomyelitis, postimmunization
Use additional code to identify the vaccine (T50.A-, T50.B-, T50.Z-)
G04.1 Tropical spastic paraplegia
G04.2 Bacterial meningoencephalitis and meningomyelitis, not elsewhere classified
G04.3 Acute necrotizing hemorrhagic encephalopathy
Excludes1: acute disseminated encephalitis and encephalomyelitis (G04.0-)
G04.30 Postinfectious acute necrotizing hemorrhagic encephalopathy
Acute necrotizing hemorrhagic encephalopathy NOS
G04.31 Postimmunization acute necrotizing hemorrhagic encephalopathy
Use additional code to identify the vaccine (T50.A-, T50.B-, T50.Z-)
G04.8 Other encephalitis, myelitis and encephalomyelitis
G04.81 Other encephalitis and encephalomyelitis
Noninfectious acute disseminated encephalomyelitis (noninfectious ADEM)
G04.89 Other myelitis
G04.9 Encephalitis, myelitis and encephalomyelitis, unspecified
G04.90 Encephalitis and encephalomyelitis, unspecified
Ventriculitis (cerebral) NOS
G04.91 Myelitis, unspecified

G05 Encephalitis, myelitis and encephalomyelitis in diseases classified elsewhere[edit]

Code first underlying disease, such as:
poliovirus (A80.-)
suppurative otitis media (H66.01-H66.4)
trichinellosis (B75)
Excludes1: encephalitis, myelitis and encephalomyelitis (in):
adenoviral (A85.1)
cytomegaloviral (B25.8)
enteroviral (A85.0)
herpesviral [herpes simplex] (B00.4)
listerial (A32.12)
measles (B05.0)
meningococcal (A39.81)
mumps (B26.2)
postchickenpox (B01.1)
rubella (B06.01)
systemic lupus erythematosus (M32.19)
toxoplasmosis (B58.2)
congenital (P37.1)
zoster (B02.0)
eosinophilic meningoencephalitis (B83.2)
G05.3 Encephalitis and encephalomyelitis in diseases classified elsewhere
Meningoencephalitis in diseases classified elsewhere
G05.4 Myelitis in diseases classified elsewhere
Meningomyelitis in diseases classified elsewhere
G06 Intracranial and intraspinal abscess and granuloma
Use additional code (B95-B97) to identify infectious agent.

G06.0 Intracranial abscess and granuloma[edit]

Brain [any part] abscess (embolic)
Cerebellar abscess (embolic)
Cerebral abscess (embolic)
Intracranial epidural abscess or granuloma
Intracranial extradural abscess or granuloma
Intracranial subdural abscess or granuloma
Otogenic abscess (embolic)
Excludes1: tuberculous intracranial abscess and granuloma (A17.81)
G06.1 Intraspinal abscess and granuloma
Abscess (embolic) of spinal cord [any part]
Intraspinal epidural abscess or granuloma
Intraspinal extradural abscess or granuloma
Intraspinal subdural abscess or granuloma
Excludes1: tuberculous intraspinal abscess and granuloma (A17.81)
G06.2 Extradural and subdural abscess, unspecified

G07 Intracranial and intraspinal abscess and granuloma in diseases classified elsewhere[edit]

Code first, underlying disease, such as:
schistosomiasis granuloma of brain (B65.-)
Excludes1: abscess of brain:
amebic (A06.6)
chromomycotic (B43.1)
gonococcal (A54.82)
tuberculous (A17.81)
tuberculoma of meninges (A17.1)

G08 Intracranial and intraspinal phlebitis and thrombophlebitis[edit]

Includes septic embolism of intracranial or intraspinal venous sinuses and veins
septic endophlebitis of intracranial or intraspinal venous sinuses and veins
septic phlebitis of intracranial or intraspinal venous sinuses and veins
septic thrombophlebitis of intracranial or intraspinal venous sinuses and veins
septic thrombosis of intracranial or intraspinal venous sinuses and veins
Excludes1: intracranial phlebitis and thrombophlebitis complicating:
abortion, ectopic or molar pregnancy (O00-O07, O08.7)
pregnancy, childbirth and the puerperium (O22.5, O87.3)
nonpyogenic intracranial phlebitis and thrombophlebitis (I67.6)
nonpyogenic intraspinal phlebitis and thrombophlebitis (G95.1)

G09 Sequelae of inflammatory diseases of central nervous system[edit]

Note: Category G09 is to be used to indicate conditions whose primary classification is to G00-G08 as the cause of sequelae, themselves classifiable elsewhere. The "sequelae" include conditions specified as residuals.
Code first condition resulting from (sequela) of inflammatory diseases of central nervous system

Systemic atrophies primarily affecting the central nervous system (G10-G14)[edit]

G10 Huntington's disease[edit]

Includes Huntington's chorea
Huntington's dementia

G11 Hereditary ataxia[edit]

Excludes2: cerebral palsy (G80.-)
hereditary and idiopathic neuropathy (G60.-)
metabolic disorders (E70-E90)
G11.0 Congenital nonprogressive ataxia
G11.1 Early-onset cerebellar ataxia
Early-onset cerebellar ataxia with essential tremor
Early-onset cerebellar ataxia with myoclonus [Hunt's ataxia]
Early-onset cerebellar ataxia with retained tendon reflexes
Friedreich's ataxia (autosomal recessive)
X-linked recessive spinocerebellar ataxia
G11.2 Late-onset cerebellar ataxia
G11.3 Cerebellar ataxia with defective DNA repair
Ataxia telangiectasia [Louis-Bar]
Excludes2: Cockayne's syndrome (Q87.1)
other disorders of purine and pyrimidine metabolism (E79.-)
xeroderma pigmentosum (Q82.1)
G11.4 Hereditary spastic paraplegia
G11.8 Other hereditary ataxias
G11.9 Hereditary ataxia, unspecified
Hereditary cerebellar ataxia NOS
Hereditary cerebellar degeneration
Hereditary cerebellar disease
Hereditary cerebellar syndrome

G12 Spinal muscular atrophy and related syndromes[edit]

G12.0 Infantile spinal muscular atrophy, type I [Werdnig-Hoffman]
G12.1 Other inherited spinal muscular atrophy
Adult form spinal muscular atrophy
Childhood form, type II spinal muscular atrophy
Distal spinal muscular atrophy
Juvenile form, type III spinal muscular atrophy [Kugelberg-Welander]
Progressive bulbar palsy of childhood [Fazio-Londe]
Scapuloperoneal form spinal muscular atrophy
G12.2 Motor neuron disease
G12.20 Motor neuron disease, unspecified
G12.21 Amyotrophic lateral sclerosis
Progressive spinal muscle atrophy
G12.22 Progressive bulbar palsy
G12.29 Other motor neuron disease
Familial motor neuron disease
Primary lateral sclerosis
G12.8 Other spinal muscular atrophies and related syndromes
G12.9 Spinal muscular atrophy, unspecified

G13 Systemic atrophies primarily affecting central nervous system in diseases classified elsewhere[edit]

G13.0 Paraneoplastic neuromyopathy and neuropathy
Carcinomatous neuromyopathy
Sensorial paraneoplastic neuropathy [Denny Brown]
Code first underlying neoplasm (C00-D48)
G13.1 Other systemic atrophy primarily affecting central nervous system in neoplastic disease
Paraneoplastic limbic encephalopathy
Code first underlying neoplasm (C00-D48)
G13.8 Systemic atrophy primarily affecting central nervous system in other diseases classified elsewhere
Code first underlying disease, such as:
cerebellar ataxia (in):
hypothyroidism (E03.-)
myxedematous congenital iodine deficiency (E00.1)

G14 Postpolio syndrome[edit]

Postpolio myelitic syndrome
Excludes1: sequelae of poliomyelitis (B91)

Extrapyramidal and movement disorders (G20-G26)[edit]

G20 Parkinson's disease[edit]

Includes hemiparkinsonism
idiopathic Parkinsonism or Parkinson's disease
paralysis agitans
Parkinsonism or Parkinson's disease NOS
primary Parkinsonism or Parkinson's disease
Excludes1: dementia with Parkinsonism (G31.83)

G21 Secondary parkinsonism[edit]

Excludes1: dementia with Parkinsonism (G31.83)
Huntington's disease (G10)
Shy-Drager syndrome (G90.3)
syphilitic Parkinsonism (A52.19)
G21.0 Malignant neuroleptic syndrome
Code first (T43.3-T43.5) to identify drug
Excludes1: neuroleptic induced parkinsonism (G21.11)
G21.1 Other drug-induced secondary parkinsonism
G21.11 Neuroleptic induced parkinsonism
Code first (T43.3-T43.5) to identify drug
Excludes1: malignant neuroleptic syndrome (G21.0)
G21.19 Other drug induced secondary parkinsonism
Code first (T36-T50) to identify drug
G21.2 Secondary parkinsonism due to other external agents
Code first (T51-T65) to identify external agent
G21.3 Postencephalitic parkinsonism
G21.4 Vascular parkinsonism
G21.8 Other secondary parkinsonism
G21.9 Secondary parkinsonism, unspecified

G23 Other degenerative diseases of basal ganglia[edit]

Excludes2: multi-system degeneration of the autonomic nervous system (G90.3)
G23.0 Hallervorden-Spatz disease
Pigmentary pallidal degeneration
G23.1 Progressive supranuclear ophthalmoplegia [Steele-Richardson-Olszewski]
G23.2 Striatonigral degeneration
G23.8 Other specified degenerative diseases of basal ganglia
Calcification of basal ganglia
G23.9 Degenerative disease of basal ganglia, unspecified

G24 Dystonia[edit]

Includes dyskinesia
Excludes2: athetoid cerebral palsy (G80.3)
G24.0 Drug induced dystonia
Code first (T36-T50) to identify drug
G24.01 Drug induced subacute dyskinesia
Drug induced blepharospasm
Drug induced orofacial dyskinesia
Neuroleptic induced tardive dyskinesia
Tardive dyskinesia
G24.02 Drug induced acute dystonia
Acute dystonic reaction to drugs
Neuroleptic induced acute dystonia
G24.09 Other drug induced dystonia
G24.1 Genetic torsion dystonia
Dystonia deformans progressiva
Dystonia musculorum deformans
Familial torsion dystonia
Idiopathic familial dystonia
Idiopathic (torsion) dystonia NOS
(Schwalbe-) Ziehen-Oppenheim disease
G24.2 Idiopathic nonfamilial dystonia
G24.3 Spasmodic torticollis
Excludes1: congenital torticollis (Q68.0)
hysterical torticollis (F44.4)
ocular torticollis (R29.891)
psychogenic torticollis (F45.8)
torticollis NOS (M43.6)
traumatic recurrent torticollis (S13.4)
G24.4 Idiopathic orofacial dystonia
Orofacial dyskinesia
Excludes1: drug induced orofacial dyskinesia (G24.01)
G24.5 Blepharospasm
Excludes1: drug induced blepharospasm (G24.01)
G24.8 Other dystonia
Acquired torsion dystonia NOS
G24.9 Dystonia, unspecified
Dyskinesia NOS

G25 Other extrapyramidal and movement disorders[edit]

Excludes2: sleep related movement disorders (G47.6-)
G25.0 Essential tremor
Familial tremor
Excludes1: tremor NOS (R25.1)
G25.1 Drug-induced tremor
Code first (T36-T50) to identify drug
G25.2 Other specified forms of tremor
Intention tremor
G25.3 Myoclonus
Drug-induced myoclonus
Palatal myoclonus
Code first (T36-T50) to identify drug, if drug-induced
Excludes1: facial myokymia (G51.4)
myoclonic epilepsy (G40.-)
G25.4 Drug-induced chorea
Code first (T36-T50) to identify drug
G25.5 Other chorea
Chorea NOS
Excludes1: chorea NOS with heart involvement (I02.0)
Huntington's chorea (G10)
rheumatic chorea (I02.-)
Sydenham's chorea (I02.-)
G25.6 Drug induced tics and other tics of organic origin
G25.61 Drug induced tics
Code first (T36-T50) to identify drug
G25.69 Other tics of organic origin
Excludes1: habit spasm (F95.9)
tic NOS (F95.9)
Tourette?s syndrome (F95.2)
G25.7 Other and unspecified drug induced movement disorders
Code first (T36-T50) to identify drug
G25.70 Drug induced movement disorder, unspecified
G25.71 Drug induced akathisia
Drug induced acathisia
Neuroleptic induced acute akathisia
G25.79 Other drug induced movement disorders
G25.8 Other specified extrapyramidal and movement disorders
G25.81 Restless legs syndrome
G25.82 Stiff-man syndrome
G25.89 Other specified extrapyramidal and movement disorders
G25.9 Extrapyramidal and movement disorder, unspecified

G26 Extrapyramidal and movement disorders in diseases classified elsewhere[edit]

Code first underlying disease

Other degenerative diseases of the nervous system (G30-G32)[edit]

G30 Alzheimer's disease[edit]

Includes Alzheimer's dementia senile and presenile forms
Use additional code to identify:
delirium, if applicable (F05)
dementia with behavioral disturbance (F02.81)
dementia without behavioral disturbance (F02.80)
Excludes1: senile degeneration of brain NEC (G31.1)
senile dementia NOS (F03)
senility NOS (R41.81)
G30.0 Alzheimer's disease with early onset
G30.1 Alzheimer's disease with late onset
G30.8 Other Alzheimer's disease
G30.9 Alzheimer's disease, unspecified

G31 Other degenerative diseases of nervous system, not elsewhere classified[edit]

Use additional code to identify:
dementia with behavioral disturbance (F02.81)
dementia without behavioral disturbance (F02.80)
Excludes2: Reye's syndrome (G93.7)
G31.0 Frontotemporal dementia
G31.01 Pick's disease
Circumscribed brain atrophy
Progressive isolated aphasia
G31.09 Other frontotemporal dementia
Frontal dementia
G31.1 Senile degeneration of brain, not elsewhere classified
Excludes1: Alzheimer's disease (G30.-)
senility NOS (R41.81)
G31.2 Degeneration of nervous system due to alcohol
Alcoholic cerebellar ataxia
Alcoholic cerebellar degeneration
Alcoholic cerebral degeneration
Alcoholic encephalopathy
Dysfunction of the autonomic nervous system due to alcohol
Code also associated alcoholism (F10.-)
G31.8 Other specified degenerative diseases of nervous system
G31.81 Alpers disease
Grey-matter degeneration
G31.82 Leigh's disease
Subacute necrotizing encephalopathy
G31.83 Dementia with Lewy bodies
Dementia with Parkinsonism
Lewy body dementia
Lewy body disease
G31.84 Mild cognitive impairment, so stated
Excludes1: age related cognitive decline (R41.81)
altered mental status (R41.82)
cerebral degeneration (G31.9)
change in mental status (R41.82)
cognitive deficits following (sequelae of) cerebral hemorrhage or infarction (I69.01, I69.11, I69.21, I69.31, I69.81, I69.91)
cognitive impairment due to intracranial or head injury (S06.-)
dementia (F01.-, F02.-, F03)
mild memory disturbance (F06.8)
neurologic neglect syndrome (R41.4)
personality change, nonpsychotic (F68.8)
G31.89 Other specified degenerative diseases of nervous system
G31.9 Degenerative disease of nervous system, unspecified

G32 Other degenerative disorders of nervous system in diseases classified elsewhere[edit]

G32.0 Subacute combined degeneration of spinal cord in diseases classified elsewhere
Dana-Putnam syndrome
Sclerosis of spinal cord (combined) (dorsolateral) (posterolateral)
Code first underlying disease, such as:
vitamin B12 deficiency (E53.8)
anemia (D51.9)
dietary (D51.3)
pernicious (D51.0)
Excludes1: syphilitic combined degeneration of spinal cord (A52.11)
G32.8 Other specified degenerative disorders of nervous system in diseases classified elsewhere
Degenerative encephalopathy in diseases classified elsewhere
Code first underlying disease, such as:
cerebral degeneration (due to):
amyloid (E85.-)
hypothyroidism (E00.-, E03.-)
neoplasm (C00-D48)
vitamin B deficiency, except thiamine (E52-E53.-)
Excludes1: superior hemorrhagic polioencephalitis [Wernicke's encephalopathy] (E51.2)

Demyelinating diseases of the central nervous system (G35-G37)[edit]

G35 Multiple sclerosis[edit]

Includes disseminated multiple sclerosis
generalized multiple sclerosis
multiple sclerosis NOS
multiple sclerosis of brain stem
multiple sclerosis of cord

G36 Other acute disseminated demyelination[edit]

Excludes1: postinfectious encephalitis and encephalomyelitis NOS (G04.020)
G36.0 Neuromyelitis optica [Devic]
Demyelination in optic neuritis
Excludes1: optic neuritis NOS (H46)
G36.1 Acute and subacute hemorrhagic leukoencephalitis [Hurst]
G36.8 Other specified acute disseminated demyelination
G36.9 Acute disseminated demyelination, unspecified

G37 Other demyelinating diseases of central nervous system[edit]

G37.0 Diffuse sclerosis of central nervous system
Periaxial encephalitis
Schilder's disease
Excludes1: X linked adrenoleukodystrophy (E71.42-)
G37.1 Central demyelination of corpus callosum
G37.2 Central pontine myelinolysis
G37.3 Acute transverse myelitis in demyelinating disease of central nervous system
Acute transverse myelitis NOS
Acute transverse myelopathy
Excludes1: multiple sclerosis (G35)
neuromyelitis optica [Devic] (G36.0)
G37.4 Subacute necrotizing myelitis of central nervous system
G37.5 Concentric sclerosis [Balo] of central nervous system
G37.8 Other specified demyelinating diseases of central nervous system
G37.9 Demyelinating disease of central nervous system, unspecified

Episodic and paroxysmal disorders (G40-G47)[edit]

G40 Epilepsy and recurrent seizures[edit]

Note: the following terms are to be considered equivalent to intractable: pharmacoresistant (pharmacologically resistant), treatment resistant, refractory (medically) and poorly controlled
Excludes1: conversion disorder with seizures (F44.5)
convulsions NOS (R56.9)
hippocampal sclerosis (G93.81)
Landau-Kleffner syndrome (F80.3)
mesial temporal sclerosis (G93.81)
seizure (convulsive) NOS (R56.9)
seizure of newborn (P90)
temporal sclerosis (G93.81)
Todd's paralysis (G83.8)
G40.0 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset
Benign childhood epilepsy with centrotemporal EEG spikes
Childhood epilepsy with occipital EEG paroxysms
Excludes1: adult onset localization-related epilepsy (G40.1-, G40.2-)
G40.00 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, not intractable
Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset without intractability
G40.001 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, not intractable, with status epilepticus
G40.009 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, not intractable, without status epilepticus
Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset NOS
G40.01 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, intractable
G40.011 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, intractable, with status epilepticus
G40.019 Localization-related (focal) (partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset, intractable, without status epilepticus
G40.1 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures
Attacks without alteration of consciousness
Simple partial seizures developing into secondarily generalized seizures
G40.10 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, not intractable
Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures without intractability
G40.101 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, not intractable, with status epilepticus
G40.109 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, not intractable, without status epilepticus
Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures NOS
G40.11 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, intractable
G40.111 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, intractable, with status epilepticus
G40.119 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures, intractable, without status epilepticus
G40.2 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures
Attacks with alteration of consciousness, often with automatisms
Complex partial seizures developing into secondarily generalized seizures
G40.20 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, not intractable
Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures without intractability
G40.201 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, not intractable, with status epilepticus
G40.209 Localization-related (focal) (partial) symptomatic epilepsy and epileptic
syndromes with complex partial seizures, not intractable, without status epilepticus
Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures NOS
G40.21 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, intractable
G40.211 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, intractable, with status epilepticus
G40.219 Localization-related (focal) (partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures, intractable, without status epilepticus
G40.3 Generalized idiopathic epilepsy and epileptic syndromes
Benign myoclonic epilepsy in infancy
Benign neonatal convulsions (familial)
Childhood absence epilepsy [pyknolepsy]
Epilepsy with grand mal seizures on awakening
Grand mal seizure NOS
Juvenile absence epilepsy
Juvenile myoclonic epilepsy [impulsive petit mal]
Nonspecific atonic epileptic seizures
Nonspecific clonic epileptic seizures
Nonspecific myoclonic epileptic seizures
Nonspecific tonic epileptic seizures
Nonspecific tonic-clonic epileptic seizures
Petit mal seizure NOS
Code also: MERRF syndrome, if applicable, (M88.32)
G40.30 Generalized idiopathic epilepsy and epileptic syndromes, not intractable
Generalized idiopathic epilepsy and epileptic syndromes without intractability
G40.301 Generalized idiopathic epilepsy and epileptic syndromes, not intractable, with status epilepticus
G40.309 Generalized idiopathic epilepsy and epileptic syndromes, not intractable, without status epilepticus
Generalized idiopathic epilepsy and epileptic syndromes NOS
G40.31 Generalized idiopathic epilepsy and epileptic syndromes, intractable
G40.311 Generalized idiopathic epilepsy and epileptic syndromes, intractable, with status epilepticus
G40.319 Generalized idiopathic epilepsy and epileptic syndromes, intractable, without status epilepticus
G40.4 Other generalized epilepsy and epileptic syndromes
Epilepsy with myoclonic absences
Epilepsy with myoclonic-astatic seizures
Infantile spasms
Lennox-Gastaut syndrome
Salaam attacks
Symptomatic early myoclonic encephalopathy
West's syndrome
G40.40 Other generalized epilepsy and epileptic syndromes, not intractable
Other generalized epilepsy and epileptic syndromes without intractability
Other generalized epilepsy and epileptic syndromes NOS
G40.401 Other generalized epilepsy and epileptic syndromes, not intractable, with status epilepticus
G40.409 Other generalized epilepsy and epileptic syndromes, not intractable, without status epilepticus
G40.41 Other generalized epilepsy and epileptic syndromes, intractable
G40.411 Other generalized epilepsy and epileptic syndromes, intractable, with status epilepticus
G40.419 Other generalized epilepsy and epileptic syndromes, intractable, without status epilepticus
G40.5 Special epileptic syndromes
Epilepsia partialis continua [Kozhevnikof]
Epileptic seizures related to alcohol
Epileptic seizures related to drugs
Epileptic seizures related to hormonal changes
Epileptic seizures related to sleep deprivation
Epileptic seizures related to stress
G40.50 Special epileptic syndromes, not intractable
Special epileptic syndromes without intractability
G40.501 Special epileptic syndromes, not intractable, with status epilepticus
G40.509 Special epileptic syndromes, not intractable, without status epilepticus
Special epileptic syndromes NOS
G40.51 Special epileptic syndromes, intractable
G40.511 Special epileptic syndromes, intractable, with status epilepticus
G40.519 Special epileptic syndromes, intractable, without status epilepticus
G40.8 Other epilepsy and seizures
Epilepsies and epileptic syndromes undetermined as to whether they are focal or generalized
G40.80 Other epilepsy, not intractable
Other epilepsy without intractability
G40.801 Other epilepsy, not intractable, with status epilepticus
G40.809 Other epilepsy, not intractable, without status epilepticus
Other epilepsy NOS
G40.81 Other epilepsy, intractable
G40.811 Other epilepsy, intractable, with status epilepticus
G40.819 Other epilepsy, intractable, without status epilepticus
G40.89 Other seizures
Excludes1: recurrent seizures NOS (G40.909)
seizure NOS (R56.9)
G40.9 Epilepsy, unspecified
G40.90 Epilepsy, unspecified, not intractable
Epilepsy, unspecified, without intractability
G40.901 Epilepsy, unspecified, not intractable, with status epilepticus
G40.909 Epilepsy, unspecified, not intractable, without status epilepticus
Epilepsy NOS
Epileptic convulsions NOS
Epileptic fits NOS
Epileptic seizures NOS
Recurrent seizures NOS
G40.91 Epilepsy, unspecified, intractable
Intractable seizure disorder NOS
G40.911 Epilepsy, unspecified, intractable, with status epilepticus
G40.919 Epilepsy, unspecified, intractable, without status epilepticus

G43 Migraine[edit]

Note: the following terms are to be considered equivalent to intractable: pharmacoresistant (pharmacologically resistant), treatment resistant, refractory (medically) and poorly controlled
Excludes1: headache NOS (R51)
headache syndromes (G44.-)
lower half migraine (G44.00)
G43.0 Migraine without aura
Common migraine
Excludes1: chronic migraine without aura (G43.7)
G43.00 Migraine without aura, not intractable
G43.001 Migraine without aura, not intractable, with status migrainosus
G43.009 Migraine without aura, not intractable, without status migrainosus
Migraine without aura NOS
G43.01 Migraine without aura, intractable
G43.011 Migraine without aura, intractable, with status migrainosus
G43.019 Migraine without aura, intractable, without status migrainosus
G43.1 Migraine with aura
Basilar migraine
Classical migraine
Migraine equivalents
Migraine preceded or accompanied by transient focal neurological phenomena
Migraine triggered seizures
Migraine with acute-onset aura
Migraine with aura without headache (migraine equivalents)
Migraine with prolonged aura
Migraine with typical aura
Retinal migraine
Code also any associated seizure (G40.-, R56.9)
Excludes1: persistent migraine aura (G43.5-, G43.6-)
G43.10 Migraine with aura, not intractable
G43.101 Migraine with aura, not intractable, with status migrainosus
G43.109 Migraine with aura, not intractable, without status migrainosus
Migraine with aura NOS
G43.11 Migraine with aura, intractable
G43.111 Migraine with aura, intractable, with status migrainosus
G43.119 Migraine with aura, intractable, without status migrainosus
G43.4 Hemiplegic migraine
Familial migraine
Sporadic migraine
G43.40 Hemiplegic migraine, not intractable
G43.401 Hemiplegic migraine, not intractable, with status migrainosus
G43.409 Hemiplegic migraine, not intractable, without status migrainosus
Hemiplegic migraine NOS
G43.41 Hemiplegic migraine, intractable
G43.411 Hemiplegic migraine, intractable, with status migrainosus
G43.419 Hemiplegic migraine, intractable, without status migrainosus
G43.5 Persistent migraine aura without cerebral infarction
G43.50 Persistent migraine aura without cerebral infarction, not intractable
G43.501 Persistent migraine aura without cerebral infarction, not intractable, with status migrainosus
G43.509 Persistent migraine aura without cerebral infarction, not intractable, without status migrainosus
Persistent migraine aura NOS
G43.51 Persistent migraine aura without cerebral infarction, intractable
G43.511 Persistent migraine aura without cerebral infarction, intractable, with status migrainosus
G43.519 Persistent migraine aura without cerebral infarction, intractable, without status migrainosus
G43.6 Persistent migraine aura with cerebral infarction
Code also the type of cerebral infarction (I63.-)
G43.60 Persistent migraine aura with cerebral infarction, not intractable
G43.601 Persistent migraine aura with cerebral infarction, not intractable, with status migrainosus
G43.609 Persistent migraine aura with cerebral infarction, not intractable, without status migrainosus
G43.61 Persistent migraine aura with cerebral infarction, intractable
G43.611 Persistent migraine aura with cerebral infarction, intractable, with status migrainosus
G43.619 Persistent migraine aura with cerebral infarction, intractable, without status migrainosus
G43.7 Chronic migraine without aura
Transformed migraine
Excludes1: migraine without aura (G43.0-)
G43.70 Chronic migraine without aura, not intractable
G43.701 Chronic migraine without aura, not intractable, with status migrainosus
G43.709 Chronic migraine without aura, not intractable, without status migrainosus
Chronic migraine without aura NOS
G43.71 Chronic migraine without aura, intractable
G43.711 Chronic migraine without aura, intractable, with status migrainosus
G43.719 Chronic migraine without aura, intractable, without status migrainosus
G43.a Cyclical vomiting
G43.a0 Cyclical vomiting, not intractable
G43.a01 Cyclical vomiting, not intractable, with status migrainosus
G43.a09 Cyclical vomiting, not intractable, without status migrainosus
Cyclical vomiting NOS
G43.a1 Cyclical vomiting, intractable
G43.a11 Cyclical vomiting, intractable, with status migrainosus
G43.a19 Cyclical vomiting, intractable, without status migrainosus
G43.b Ophthalmoplegic migraine
G43.b0 Ophthalmoplegic migraine, not intractable
G43.b01 Ophthalmoplegic migraine, not intractable, with status migrainosus
G43.b09 Ophthalmoplegic migraine, not intractable, without status migrainosus
Ophthalmoplegic migraine NOS
G43.b1 Ophthalmoplegic migraine, intractable
G43.b11 Ophthalmoplegic migraine, intractable, with status migrainosus
G43.b19 Ophthalmoplegic migraine, intractable, without status migrainosus
G43.c Periodic headache syndromes in child or adult
G43.c0 Periodic headache syndromes in child or adult, not intractable
G43.c01 Periodic headache syndromes in child or adult, not intractable, with status migrainosus
G43.c09 Periodic headache syndromes in child or adult, not intractable, without status migrainosus
Periodic headache syndromes in child or adult NOS
G43.c1 Periodic headache syndromes in child or adult, intractable
G43.c11 Periodic headache syndromes in child or adult, intractable, with status migrainosus
G43.c19 Periodic headache syndromes in child or adult, intractable, without status migrainosus
G43.d Menstrual migraine
Menstrual headache
Menstrually related migraine
Pre-menstrual headache
Pre-menstrual migraine
Pure menstrual migarine
Code also associated premenstrual tension syndrome (N94.3)
G43.d0 Menstrual migraine, not intractable
G43.d01 Menstrual migraine, not intractable, with status migrainosus
G43.d09 Menstrual migraine, not intractable, without status migrainosus
Menstrual migraine NOS
G43.d1 Menstrual migraine, intractable
G43.d11 Menstrual migraine, intractable, with status migrainosus
G43.d19 Menstrual migraine, intractable, without status migrainosus
G43.8 Other migraine
G43.80 Other migraine, not intractable
G43.801 Other migraine, not intractable, with status migrainosus
G43.809 Other migraine, not intractable, without status migrainosus
G43.81 Other migraine, intractable
G43.811 Other migraine, intractable, with status migrainosus
G43.819 Other migraine, intractable, without status migrainosus
G43.9 Migraine, unspecified
G43.90 Migraine, unspecified, not intractable
G43.901 Migraine, unspecified, not intractable, with status migrainosus
Status migrainosus NOS
G43.909 Migraine, unspecified, not intractable, without status migrainosus
Migraine NOS
G43.91 Migraine, unspecified, intractable
G43.911 Migraine, unspecified, not intractable, with status migrainosus
G43.919 Migraine, unspecified, not intractable, without status migrainosus

G44 Other headache syndromes[edit]

Excludes1: headache NOS (R51)
Excludes2: atypical facial pain (G50.1)
headache due to lumbar puncture (G97.1)
migraines (G43.-)
trigeminal neuralgia (G50.0)
G44.0 Cluster headaches and other trigeminal autonomic cephalgias (TAC)
G44.00 Cluster headache syndrome, unspecified
Ciliary neuralgia
Cluster headache NOS
Histamine cephalgia
Lower half migraine
Migrainous neuralgia
G44.001 Cluster headache syndrome, unspecified, intractable
G44.009 Cluster headache syndrome, unspecified, not intractable
Cluster headache syndrome NOS
G44.01 Episodic cluster headache
G44.011 Episodic cluster headache, intractable
G44.019 Episodic cluster headache, not intractable
Episodic cluster headache NOS
G44.02 Chronic cluster headache
G44.021 Chronic cluster headache, intractable
G44.029 Chronic cluster headache, not intractable
Chronic cluster headache NOS
G44.03 Episodic paroxysmal hemicrania
Paroxysmal hemicrania NOS
G44.031 Episodic paroxysmal hemicrania, intractable
G44.039 Episodic paroxysmal hemicrania, not intractable
Episodic paroxysmal hemicrania NOS
G44.04 Chronic paroxysmal hemicrania
G44.041 Chronic paroxysmal hemicrania, intractable
G44.049 Chronic paroxysmal hemicrania, not intractable
Chronic paroxysmal hemicrania NOS
G44.05 Short lasting unilateral neuralgiform headache with conjunctival injection and tearing (SUNCT)
G44.051 Short lasting unilateral neuralgiform headache with conjunctival injection and tearing (SUNCT), intractable
G44.059 Short lasting unilateral neuralgiform headache with conjunctival injection and tearing (SUNCT), not intractable
Short lasting unilateral neuralgiform headache with conjunctival injection and tearing (SUNCT) NOS
G44.09 Other trigeminal autonomic cephalgias (TAC)
G44.091 Other trigeminal autonomic cephalgias (TAC), intractable
G44.099 Other trigeminal autonomic cephalgias (TAC), not intractable
G44.1 Vascular headache, not elsewhere classified
G44.10 Vascular headache, not elsewhere classified, not intractable
Vascular headache NOS
G44.11 Vascular headache, not elsewhere classified, intractable
G44.2 Tension-type headache
G44.20 Tension-type headache, unspecified
G44.201 Tension-type headache, unspecified, intractable
G44.209 Tension-type headache, unspecified, not intractable
Tension headache NOS
G44.21 Episodic tension-type headache
G44.211 Episodic tension-type headache, intractable
G44.219 Episodic tension-type headache, not intractable
Episodic tension-type headache NOS
G44.22 Chronic tension-type headache
G44.221 Chronic tension-type headache, intractable
G44.229 Chronic tension-type headache, not intractable
Chronic tension-type headache NOS
G44.3 Post-traumatic headache
Code first: postconcussional syndrome (F07.81)
G44.30 Post-traumatic headache, unspecified
G44.301 Post-traumatic headache, unspecified, intractable
G44.309 Post-traumatic headache, unspecified, not intractable
Post-traumatic headache NOS
G44.31 Acute post-traumatic headache
G44.311 Acute post-traumatic headache, intractable
G44.319 Acute post-traumatic headache, not intractable
Acute post-traumatic headache NOS
G44.32 Chronic post-traumatic headache
G44.321 Chronic post-traumatic headache, intractable
G44.329 Chronic post-traumatic headache, not intractable
Chronic post-traumatic headache NOS
G44.4 Drug-induced headache, not elsewhere classified
Medication overuse headache
Code first (T36-T50) to identify drug
G44.40 Drug-induced headache, not elsewhere classified, not intractable
G44.41 Drug-induced headache, not elsewhere classified, intractable
G44.5 Complicated headache syndromes
G44.51 Hemicrania continua
G44.52 New daily persistent headache (NDPH)
G44.53 Primary thunderclap headache
G44.59 Other complicated headache syndrome
G44.8 Other specified headache syndromes
G44.81 Hypnic headache
G44.82 Headache associated with sexual activity
Orgasmic headache
Preorgasmic headache
G44.83 Primary cough headache
G44.84 Primary exertional headache
G44.85 Primary stabbing headache
G44.89 Other headache syndrome

G45 Transient cerebral ischemic attacks and related syndromes[edit]

Excludes1: neonatal cerebral ischemia (P91.0)
transient retinal artery occlusion (H34.0-)
G45.0 Vertebro-basilar artery syndrome
G45.1 Carotid artery syndrome (hemispheric)
G45.2 Multiple and bilateral precerebral artery syndromes
G45.3 Amaurosis fugax
G45.4 Transient global amnesia
Excludes1: amnesia NOS (R41.3)
G45.8 Other transient cerebral ischemic attacks and related syndromes
G45.9 Transient cerebral ischemic attack, unspecified
Spasm of cerebral artery
TIA
Transient cerebral ischemia NOS

G46 Vascular syndromes of brain in cerebrovascular diseases[edit]

Code first underlying cerebrovascular disease (I60-I69)
G46.0 Middle cerebral artery syndrome
G46.1 Anterior cerebral artery syndrome
G46.2 Posterior cerebral artery syndrome
G46.3 Brain stem stroke syndrome
Benedikt syndrome
Claude syndrome
Foville syndrome
Millard-Gubler syndrome
Wallenberg syndrome
Weber syndrome
G46.4 Cerebellar stroke syndrome
G46.5 Pure motor lacunar syndrome
G46.6 Pure sensory lacunar syndrome
G46.7 Other lacunar syndromes
G46.8 Other vascular syndromes of brain in cerebrovascular diseases

G47 Sleep disorders[edit]

Excludes2: nightmares (F51.5)
nonorganic sleep disorders (F51.-)
sleep terrors (F51.4)
sleepwalking (F51.3)
G47.0 Insomnia
Excludes2: alcohol related insomnia (F10.182, F10.282, F10.982)
drug related insomnia (F11.182, F11.282, F11.982, F13.182, F13.282, F13.982, F14.182, F14.282, F14.982, F15.182, F15.282, F15.982, F19.182, F19.282, F19.982)
idiopathic insomnia (F51.01)
insomnia due to a mental disorder (F51.05)
insomnia not due to a substance or known physiological condition (F51.0-)
nonorganic insomnia (F51.0-)
primary insomnia (F51.01)
sleep apnea (G47.3-)
G47.00 Insomnia, unspecified
Insomnia NOS
G47.01 Insomnia due to medical condition
Code also associated medical condition
G47.09 Other insomnia
G47.1 Hypersomnia
Excludes2: alcohol-related hypersomnia (F10.182, F10.282, F10.982)
drug-related hypersomnia (F11.182, F11.282, F11.982, F13.182, F13.282, F13.982, F14.182, F14.282, F14.982, F15.182, F15.282, F15.982, F19.182, F19.282, F19.982)
hypersomnia due to a mental disorder (F51.13)
hypersomnia not due to a substance or known physiological condition (F51.11)
primary hypersomnia (F51.11)
sleep apnea (G47.3-)
G47.10 Hypersomnia, unspecified
Hypersomnia NOS
G47.11 Idiopathic hypersomnia with long sleep time
Idiopathic hypersomnia NOS
G47.12 Idiopathic hypersomnia without long sleep time
G47.13 Recurrent hypersomnia
Kleine-Levin syndrome
Menstrual related hypersomnia
G47.14 Hypersomnia due to medical condition
Code also associated medical condition
G47.19 Other hypersomnia
G47.2 Circadian rhythm sleep disorders
Disorders of the sleep wake schedule
Inversion of nyctohemeral rhythm
Inversion of sleep rhythm
G47.20 Circadian rhythm sleep disorder, unspecified type
Sleep wake schedule disorder NOS
G47.21 Circadian rhythm sleep disorder, delayed sleep phase type
Delayed sleep phase syndrome
G47.22 Circadian rhythm sleep disorder, advanced sleep phase type
G47.23 Circadian rhythm sleep disorder, irregular sleep wake type
Irregular sleep-wake pattern
G47.24 Circadian rhythm sleep disorder, free running type
G47.25 Circadian rhythm sleep disorder, jet lag type
G47.26 Circadian rhythm sleep disorder, shift work type
G47.27 Circadian rhythm sleep disorder in conditions classified elsewhere
Code first underlying condition
G47.29 Other circadian rhythm sleep disorder
G47.3 Sleep apnea
Code also any associated underlying condition
Excludes1: apnea NOS R06.81
Cheyne-Stokes breathing (R06.3)
pickwickian syndrome (E66.2)
sleep apnea of newborn (P28.3)
G47.30 Sleep apnea, unspecified
Sleep apnea NOS
G47.31 Primary central sleep apnea
G47.32 High altitude periodic breathing
G47.33 Obstructive sleep apnea (adult) (pediatric)
G47.34 Idiopathic sleep related nonobstructive alveolar hypoventilation
Sleep related hypoxia
G47.35 Congenital central alveolar hypoventilation syndrome
G47.36 Sleep related hypoventilation in conditions classified elsewhere
Sleep related hypoxemia in conditions classified elsewhere
Code first underlying condition
G47.37 Central sleep apnea in conditions classified elsewhere
Code first underlying condition
G47.39 Other sleep apnea
G47.4 Narcolepsy and cataplexy
G47.41 Narcolepsy
G47.411 Narcolepsy with cataplexy
G47.419 Narcolepsy without cataplexy
Narcolepsy NOS
G47.42 Narcolepsy in conditions classified elsewhere
G47.421 Narcolepsy in conditions classified elsewhere with cataplexy
G47.429 Narcolepsy in conditions classified elsewhere without cataplexy
G47.5 Parasomnia
Excludes1: alcohol induced parasomnia (F10.182, F10.282, F10.982)
drug induced parasomnia (F11.182, F11.282, F11.982, F13.182, F13.282, F13.982, F14.182, F14.282, F14.982, F15.182, F15.282, F15.982, F19.182, F19.282, F19.982)
parasomnia not due to a substance or known physiological condition (F51.8)
G47.50 Parasomnia, unspecified
Parasomnia NOS
G47.51 Confusional arousals
G47.52 REM sleep behavior disorder
G47.53 Recurrent isolated sleep paralysis
G47.54 Parasomnia in conditions classified elsewhere
Code first underlying condition
G47.59 Other parasomnia
G47.6 Sleep related movement disorders
Excludes2: restless legs syndrome (G25.81)
G47.61 Periodic limb movement disorder
G47.62 Sleep related leg cramps
G47.63 Sleep related bruxism
Excludes1: psychogenic bruxism (F45.8)
G47.69 Other sleep related movement disorders
G47.8 Other sleep disorders
G47.9 Sleep disorder, unspecified
Sleep disorder NOS

Nerve, nerve root and plexus disorders (G50-G59)[edit]

Excludes1: current traumatic nerve, nerve root and plexus disorders - see Injury, nerve by body region
neuralgia NOS (M79.2)
neuritis NOS (M79.2)
peripheral neuritis in pregnancy (O26.82-)
radiculitis NOS (M54.1-)

G50 Disorders of trigeminal nerve[edit]

Includes disorders of 5th cranial nerve
G50.0 Trigeminal neuralgia
Syndrome of paroxysmal facial pain
Tic douloureux
G50.1 Atypical facial pain
G50.8 Other disorders of trigeminal nerve
G50.9 Disorder of trigeminal nerve, unspecified

G51 Facial nerve disorders[edit]

Includes disorders of 7th cranial nerve
G51.0 Bell's palsy
Facial palsy
G51.1 Geniculate ganglionitis
Excludes1: postherpetic geniculate ganglionitis (B02.21)
G51.2 Melkersson's syndrome
Melkersson-Rosenthal syndrome
G51.3 Clonic hemifacial spasm
G51.4 Facial myokymia
G51.8 Other disorders of facial nerve
G51.9 Disorder of facial nerve, unspecified

G52 Disorders of other cranial nerves[edit]

Excludes2: disorders of acoustic [8th] nerve (H93.3)
disorders of optic [2nd] nerve (H46, H47.0)
paralytic strabismus due to nerve palsy (H49.0-H49.2)
G52.0 Disorders of olfactory nerve
Disorders of 1st cranial nerve
G52.1 Disorders of glossopharyngeal nerve
Disorder of 9th cranial nerve
Glossopharyngeal neuralgia
G52.2 Disorders of vagus nerve
Disorders of pneumogastric [10th] nerve
G52.3 Disorders of hypoglossal nerve
Disorders of 12th cranial nerve
G52.7 Disorders of multiple cranial nerves
Polyneuritis cranialis
G52.8 Disorders of other specified cranial nerves
G52.9 Cranial nerve disorder, unspecified

G53 Cranial nerve disorders in diseases classified elsewhere[edit]

Code first underlying disease, such as:
neoplasm (C00-D48)
Excludes1: multiple cranial nerve palsy in sarcoidosis (D86.82)
multiple cranial nerve palsy in syphilis (A52.15)
postherpetic geniculate ganglionitis (B02.21)
postherpetic trigeminal neuralgia (B02.22)

G54 Nerve root and plexus disorders[edit]

Excludes1: current traumatic nerve root and plexus disorders - see nerve injury by body region
intervertebral disc disorders (M50-M51)
neuralgia or neuritis NOS (M79.2)
neuritis or radiculitis:
brachial NOS (M54.13)
lumbar NOS (M54.16)
lumbosacral NOS (M54.17)
thoracic NOS (M54.14)
radiculitis NOS (M54.10)
radiculopathy NOS (M54.10)
spondylosis (M47.-)
G54.0 Brachial plexus disorders
Thoracic outlet syndrome
G54.1 Lumbosacral plexus disorders
G54.2 Cervical root disorders, not elsewhere classified
G54.3 Thoracic root disorders, not elsewhere classified
G54.4 Lumbosacral root disorders, not elsewhere classified
G54.5 Neuralgic amyotrophy
Parsonage-Aldren-Turner syndrome
Shoulder-girdle neuritis
Excludes1: neuralgic amyotrophy in diabetes mellitus (E09-E13 with .44)
G54.6 Phantom limb syndrome with pain
G54.7 Phantom limb syndrome without pain
Phantom limb syndrome NOS
G54.8 Other nerve root and plexus disorders
G54.9 Nerve root and plexus disorder, unspecified

G55 Nerve root and plexus compressions in diseases classified elsewhere[edit]

Code first underlying disease, such as:
neoplasm (C00-D48)
Excludes1: nerve root compression (due to) (in):
ankylosing spondylitis (M45.-)
dorsopathies (M53.-, M54.-)
intervertebral disc disorders (M50.1.-, M51.1.-)
spondylopathies (M46.-, M48.-)
spondylosis (M47.0-M47.2.-)

G56 Mononeuropathies of upper limb[edit]

Excludes1: current traumatic nerve disorder - see nerve injury by body region
G56.0 Carpal tunnel syndrome
G56.00 Carpal tunnel syndrome, unspecified side
G56.01 Carpal tunnel syndrome, right side
G56.02 Carpal tunnel syndrome, left side
G56.1 Other lesions of median nerve
G56.10 Other lesions of median nerve, unspecified side
G56.11 Other lesions of median nerve, right side
G56.12 Other lesions of median nerve, left side
G56.2 Lesion of ulnar nerve
Tardy ulnar nerve palsy
G56.20 Lesion of ulnar nerve, unspecified side
G56.21 Lesion of ulnar nerve, right side
G56.22 Lesion of ulnar nerve, left side
G56.3 Lesion of radial nerve
G56.30 Lesion of radial nerve, unspecified side
G56.31 Lesion of radial nerve, right side
G56.32 Lesion of radial nerve, left side
G56.4 Causalgia of upper limb
Complex regional pain syndrome II of upper limb
Excludes1: complex regional pain syndrome I of lower limb (G90.52-)
complex regional pain syndrome I of upper limb (G90.51-)
complex regional pain syndrome II of lower limb (G57.7-)
reflex sympathetic dystrophy of lower limb (G90.52-)
reflex sympathetic dystrophy of upper limb (G90.51-)
G56.40 Causalgia of upper limb, unspecified side
G56.41 Causalgia of upper limb, right side
G56.42 Causalgia of upper limb, left side
G56.8 Other mononeuropathies of upper limb
Interdigital neuroma of upper limb
G56.80 Other mononeuropathies of upper limb, unspecified side
G56.81 Other mononeuropathies of upper limb, right side
G56.82 Other mononeuropathies of upper limb, left side
G56.9 Mononeuropathy of upper limb, unspecified
G56.90 Mononeuropathy of upper limb, unspecified, unspecified side
G56.91 Mononeuropathy of upper limb, unspecified, right side
G56.92 Mononeuropathy of upper limb, unspecified, left side

G57 Mononeuropathies of lower limb[edit]

Excludes1: current traumatic nerve disorder - see nerve injury by body region
G57.0 Lesion of sciatic nerve
Excludes1: sciatica NOS (M54.3-)
Excludes2: sciatica attributed to intervertebral disc disorder (M51.1.-)
G57.00 Lesion of sciatic nerve, unspecified side
G57.01 Lesion of sciatic nerve, right side
G57.02 Lesion of sciatic nerve, left side
G57.1 Meralgia paresthetica
Lateral cutaneous nerve of thigh syndrome
G57.10 Meralgia paresthetica, unspecified side
G57.11 Meralgia paresthetica, right side
G57.12 Meralgia paresthetica, left side
G57.2 Lesion of femoral nerve
G57.20 Lesion of femoral nerve, unspecified side
G57.21 Lesion of femoral nerve, right side
G57.22 Lesion of femoral nerve, left side
G57.3 Lesion of lateral popliteal nerve
Peroneal nerve palsy
G57.30 Lesion of lateral popliteal nerve, unspecified side
G57.31 Lesion of lateral popliteal nerve, right side
G57.32 Lesion of lateral popliteal nerve, left side
G57.4 Lesion of medial popliteal nerve
G57.40 Lesion of medial popliteal nerve, unspecified side
G57.41 Lesion of medial popliteal nerve, right side
G57.42 Lesion of medial popliteal nerve, left side
G57.5 Tarsal tunnel syndrome
G57.50 Tarsal tunnel syndrome, unspecified side
G57.51 Tarsal tunnel syndrome, right side
G57.52 Tarsal tunnel syndrome, left side
G57.6 Lesion of plantar nerve
Morton's metatarsalgia
G57.60 Lesion of plantar nerve, unspecified side
G57.61 Lesion of plantar nerve, right side
G57.62 Lesion of plantar nerve, left side
G57.7 Causalgia of lower limb
Complex regional pain syndrome II of lower limb
Excludes1: complex regional pain syndrome I of lower limb (G90.52-)
complex regional pain syndrome I of upper limb (G90.51-)
complex regional pain syndrome II of upper limb (G56.4-)
reflex sympathetic dystrophy of lower limb (G90.52-)
reflex sympathetic dystrophy of upper limb (G90.51-)
G57.70 Causalgia of lower limb, unspecified side
G57.71 Causalgia of lower limb, right side
G57.72 Causalgia of lower limb, left side
G57.8 Other mononeuropathies of lower limb
Interdigital neuroma of lower limb
G57.80 Other mononeuropathies of lower limb, unspecified side
G57.81 Other mononeuropathies of lower limb, right side
G57.82 Other mononeuropathies of lower limb, left side
G57.9 Mononeuropathy of lower limb, unspecified
G57.90 Mononeuropathy of lower limb, unspecified, unspecified side
G57.91 Mononeuropathy of lower limb, unspecified, right side
G57.92 Mononeuropathy of lower limb, unspecified, left side

G58 Other mononeuropathies[edit]

G58.0 Intercostal neuropathy
G58.7 Mononeuritis multiplex
G58.8 Other specified mononeuropathies
G58.9 Mononeuropathy, unspecified

G59 Mononeuropathy in diseases classified elsewhere[edit]

Code first underlying disease
Excludes1: diabetic mononeuropathy (E09-E14 with .41)
syphilitic nerve paralysis (A52.19)
syphilitic neuritis (A52.15)
tuberculous mononeuropathy (A17.83)

Polyneuropathies and other disorders of the peripheral nervous system (G60-G64)[edit]

Excludes1: neuralgia NOS (M79.2)
neuritis NOS (M79.2)
peripheral neuritis in pregnancy (O26.82-)
radiculitis NOS (M54.10)

G60 Hereditary and idiopathic neuropathy[edit]

G60.0 Hereditary motor and sensory neuropathy
Charcot-Marie-Tooth disease
Déjérine-Sottas disease
Hereditary motor and sensory neuropathy, types I-IV
Hypertrophic neuropathy of infancy
Peroneal muscular atrophy (axonal type) (hypertrophic type)
Roussy-Levy syndrome
G60.1 Refsum's disease
Infantile Refsum disease
G60.2 Neuropathy in association with hereditary ataxia
G60.3 Idiopathic progressive neuropathy
G60.8 Other hereditary and idiopathic neuropathies
Dominantly inherited sensory neuropathy
Morvan's disease
Nelaton's syndrome
Recessively inherited sensory neuropathy
G60.9 Hereditary and idiopathic neuropathy, unspecified

G61 Inflammatory polyneuropathy[edit]

G61.0 Guillain-Barre syndrome
Acute (post-)infective polyneuritis
Miller Fisher Syndrome
G61.1 Serum neuropathy
Code first (T50.9-) to identify serum
G61.8 Other inflammatory polyneuropathies
G61.81 Chronic inflammatory demyelinating polyneuritis
G61.89 Other inflammatory polyneuropathies
G61.9 Inflammatory polyneuropathy, unspecified

G62 Other and unspecified polyneuropathies[edit]

G62.0 Drug-induced polyneuropathy
Code first (T36-T50) to identify drug
G62.1 Alcoholic polyneuropathy
G62.2 Polyneuropathy due to other toxic agents
Code first (T51-T65) to identify toxic agent.
G62.8 Other specified polyneuropathies
G62.81 Critical illness polyneuropathy
Acute motor neuropathy
G62.82 Radiation-induced polyneuropathy
Use additional external cause code (W88-W90, X39.0-) to identify cause
G62.89 Other specified polyneuropathies
G62.9 Polyneuropathy, unspecified
Neuropathy NOS

G63 Polyneuropathy in diseases classified elsewhere[edit]

Code first underlying disease, such as:
amyloidosis (E85.-)
endocrine disease, except diabetes (E00-E07, E15-E16, E20-E34)
metabolic diseases (E70-E89)
neoplasm (C00-D48)
nutritional deficiency (E40-E64)
Excludes1: polyneuropathy (in):
diabetes mellitus (E09-E13 with .42)
diphtheria (A36.83)
infectious mononucleosis (B27.0-B27.9 with 1)
Lyme disease (A69.22)
mumps (B26.84)
postherpetic (B02.23)
rheumatoid arthritis (M05.33)
scleroderma (M34.83)
systemic lupus erythematosus (M32.19)

G64 Other disorders of peripheral nervous system[edit]

Disorder of peripheral nervous system NOS

G65 Sequelae of inflammatory and toxic polyneuropathies[edit]

Code first condition resulting from (sequela) of inflammatory and toxic polyneuropathies
G65.0 Sequelae of Guillain-Barr? syndrome
G65.1 Sequelae of other inflammatory polyneuropathy
G65.2 Sequelae of toxic polyneuropathy

Diseases of myoneural junction and muscle (G70-G73)[edit]

G70 Myasthenia gravis and other myoneural disorders[edit]

Excludes1: botulism (A05.1, A48.51- A48.52)
transient neonatal myasthenia gravis (P94.0)
G70.0 Myasthenia gravis
G70.00 Myasthenia gravis without (acute) exacerbation
Myasthenia gravis NOS
G70.01 Myasthenia gravis with (acute) exacerbation
Myasthenia gravis in crisis
G70.1 Toxic myoneural disorders
Code first (T51-T65) to identify toxic agent.
G70.2 Congenital and developmental myasthenia
G70.8 Other specified myoneural disorders
G70.9 Myoneural disorder, unspecified

G71 Primary disorders of muscles[edit]

Excludes2: arthrogryposis multiplex congenita (Q74.3)
metabolic disorders (E70-E90)
myositis (M60.-)
G71.0 Muscular dystrophy
Autosomal recessive, childhood type, muscular dystrophy resembling Duchenne or Becker muscular dystrophy
Benign [Becker] muscular dystrophy
Benign scapuloperoneal muscular dystrophy with early contractures [Emery-Dreifuss]
Distal muscular dystrophy
Facioscapulohumeral muscular dystrophy
Limb-girdle muscular dystrophy
Ocular muscular dystrophy
Oculopharyngeal muscular dystrophy
Scapuloperoneal muscular dystrophy
Severe [Duchenne] muscular dystrophy
Excludes1: congenital muscular dystrophy NOS (G71.2)
congenital muscular dystrophy with specific morphological abnormalities of the muscle fiber (G71.2)
G71.1 Myotonic disorders
G71.11 Myotonic muscular dystrophy
Dystrophia myotonica [Steinert]
Myotonia atrophica
Myotonic dystrophy
Proximal myotonic myopathy (PROMM)
Steinert disease
G71.12 Myotonia congenita
Acetazolamide responsive myotonia congenita
Dominant myotonia congenita [Thomsen disease]
Myotonia levior
Recessive myotonia congenita [Becker disease]
G71.13 Myotonic chondrodystrophy
Chondrodystrophic myotonia
Congenital myotonic chondrodystrophy
Schwartz-Jampel disease
G71.14 Drug induced myotonia
Code first (T36-T50) to identify drug
G71.19 Other specified myotonic disorders
Myotonia fluctuans
Myotonia permanens
Neuromyotonia [Isaacs]
Paramyotonia congenita (of von Eulenburg)
Pseudomyotonia
Symptomatic myotonia
G71.2 Congenital myopathies
Central core disease
Congenital muscular dystrophy NOS
Congenital muscular dystrophy with specific morphological abnormalities of the muscle fiber
Fiber-type disproportion
Minicore disease
Multicore disease
Myotubular (centronuclear) myopathy
Nemaline myopathy
Excludes1: arthrogryposis multiplex congenita (Q74.3)
G71.3 Mitochondrial myopathy, not elsewhere classified
Excludes1: Kearns-Sayre syndrome (H49.81)
Leber's disease (H47.21)
Leigh's encephalopathy (G31.82)
mitochondrial metabolism disorders (E88.4.-)
Reye's syndrome (G93.7)
G71.8 Other primary disorders of muscles
G71.9 Primary disorder of muscle, unspecified
Hereditary myopathy NOS

G72 Other and unspecified myopathies[edit]

Excludes1: arthrogryposis multiplex congenita (Q74.3)
dermatopolymyositis (M33.-)
ischemic infarction of muscle (M62.2-)
myositis (M60.-)
polymyositis (M33.2.-)
G72.0 Drug-induced myopathy
Code first (T36-T50) to identify drug
G72.1 Alcoholic myopathy
Use additional code to identify alcoholism (F10.-)
G72.2 Myopathy due to other toxic agents
Code first (T51-T65) to identify toxic agent.
G72.3 Periodic paralysis
Familial periodic paralysis
Hyperkalemic periodic paralysis (familial)
Hypokalemic periodic paralysis (familial)
Myotonic periodic paralysis (familial)
Normokalemic paralysis (familial)
Potassium sensitive periodic paralysis
Excludes1: paramyotonia congenita (of von Eulenburg) (G71.19)
G72.4 Inflammatory and immune myopathies, not elsewhere classified
G72.41 Inclusion body myositis [IBM]
G72.49 Other inflammatory and immune myopathies, not elsewhere classified
Inflammatory myopathy NOS
G72.8 Other specified myopathies
G72.81 Critical illness myopathy
Acute necrotizing myopathy
Acute quadriplegic myopathy
Intensive care (ICU) myopathy
Myopathy of critical illness
G72.89 Other specified myopathies
G72.9 Myopathy, unspecified

G73 Disorders of myoneural junction and muscle in diseases classified elsewhere[edit]

G73.1 Lambert-Eaton syndrome
Code first underlying disease, such as:
malignant neoplasm of lung (C34.-)
other neoplastic disease (C00-D48)
Excludes1: Lambert-Eaton syndrome not associated with neoplasm (G70.8)
G73.3 Myasthenic syndromes in other diseases classified elsewhere
Code first underlying disease, such as:
neoplasm (C00-D498)
thyrotoxicosis (E05.-)
G73.7 Myopathy in diseases classified elsewhere
Code first underlying disease, such as:
hyperparathyroidism (E21.0, E21.3)
hypoparathyroidism (E20.-)
glycogen storage disease (E74.0)
lipid storage disorders (E75.-)
Excludes1: myopathy in:
rheumatoid arthritis (M05.32)
sarcoidosis (D86.87)
scleroderma (M34.82)
sicca syndrome [Sj?gren] (M35.03)
systemic lupus erythematosus (M32.19)

Cerebral palsy and other paralytic syndromes (G80-G83)[edit]

G80 Cerebral palsy[edit]

Excludes1: hereditary spastic paraplegia (G11.4)
G80.0 Spastic quadriplegic cerebral palsy
Congenital spastic paralysis (cerebral)
G80.1 Spastic diplegic cerebral palsy
Spastic cerebral palsy NOS
G80.2 Spastic hemiplegic cerebral palsy
G80.3 Athetoid cerebral palsy
Double athetosis (syndrome)
Dyskinetic cerebral palsy
Dystonic cerebral palsy
Vogt disease
G80.4 Ataxic cerebral palsy
G80.8 Other cerebral palsy
Mixed cerebral palsy syndromes
G80.9 Cerebral palsy, unspecified
Cerebral palsy NOS

G81 Hemiplegia and hemiparesis[edit]

Note: This category is to be used only when hemiplegia (complete)(incomplete) is reported without further specification, or is stated to be old or
longstanding but of unspecified cause. The category is also for use in multiple coding to identify these types of hemiplegia resulting from any cause.
Excludes1: congenital cerebral palsy (G80.-)
hemiplegia and hemiparesis due to sequela of cerebrovascular disease (I69.05-, I69.15-, I69.25-, I69.35-, I69.45-, I69.85-, I69.95-)
G81.0 Flaccid hemiplegia
G81.00 Flaccid hemiplegia affecting unspecified side
G81.01 Flaccid hemiplegia affecting right dominant side
G81.02 Flaccid hemiplegia affecting left dominant side
G81.03 Flaccid hemiplegia affecting right nondominant side
G81.04 Flaccid hemiplegia affecting left nondominant side
G81.1 Spastic hemiplegia
G81.10 Spastic hemiplegia affecting unspecified side
G81.11 Spastic hemiplegia affecting right dominant side
G81.12 Spastic hemiplegia affecting left dominant side
G81.13 Spastic hemiplegia affecting right nondominant side
G81.14 Spastic hemiplegia affecting left nondominant side
G81.9 Hemiplegia, unspecified
G81.90 Hemiplegia, unspecified affecting unspecified side
G81.91 Hemiplegia, unspecified affecting right dominant side
G81.92 Hemiplegia, unspecified affecting left dominant side
G81.93 Hemiplegia, unspecified affecting right nondominant side
G81.94 Hemiplegia, unspecified affecting left nondominant side

G82 Paraplegia (paraparesis) and quadriplegia (quadriparesis)[edit]

Note: This category is to be used only when the listed conditions are reported without further specification, or are stated to be old or longstanding but of unspecified cause. The category is also for use in multiple coding to identify these conditions resulting from any cause
Excludes1: congenital cerebral palsy (G80.-)
functional quadriplegia (R53.2)
hysterical paralysis (F44.4)
G82.2 Paraplegia
Paralysis of both lower limbs NOS
Paraparesis (lower) NOS
Paraplegia (lower) NOS
G82.20 Paraplegia, unspecified
G82.21 Paraplegia, complete
G82.22 Paraplegia, incomplete
G82.5 Quadriplegia
G82.50 Quadriplegia, unspecified
G82.51 Quadriplegia, C1-C4 complete
G82.52 Quadriplegia, C1-C4 incomplete
G82.53 Quadriplegia, C5-C7 complete
G82.54 Quadriplegia, C5-C7 incomplete

G83 Other paralytic syndromes[edit]

Note: This category is to be used only when the listed conditions are reported without further specification, or are stated to be old or longstanding but of unspecified cause. The category is also for use in multiple coding to identify these conditions resulting from any cause.
Includes paralysis (complete) (incomplete), except as in G80-G82
G83.0 Diplegia of upper limbs
Diplegia (upper)
Paralysis of both upper limbs
G83.1 Monoplegia of lower limb
Paralysis of lower limb
Excludes1: monoplegia of lower limbs due to sequela of cerebrovascular disease (I69.04-, I69.14-, I69.24-, I69.34-, I69.44-, I69.84-, I69.94-)
G83.10 Monoplegia of lower limb affecting unspecified side
G83.11 Monoplegia of lower limb affecting right dominant side
G83.12 Monoplegia of lower limb affecting left dominant side
G83.13 Monoplegia of lower limb affecting right nondominant side
G83.14 Monoplegia of lower limb affecting left nondominant side
G83.2 Monoplegia of upper limb
Paralysis of upper limb
Excludes1: monoplegia of upper limbs due to sequela of cerebrovascular disease (I69.03-, I69.13-, I69.23-, I69.33-, I69.43-, I69.83-, I69.93-)
G83.20 Monoplegia of upper limb affecting unspecified side
G83.21 Monoplegia of upper limb affecting right dominant side
G83.22 Monoplegia of upper limb affecting left dominant side
G83.23 Monoplegia of upper limb affecting right nondominant side
G83.24 Monoplegia of upper limb affecting left nondominant side
G83.3 Monoplegia, unspecified
G83.30 Monoplegia, unspecified affecting unspecified side
G83.31 Monoplegia, unspecified affecting right dominant side
G83.32 Monoplegia, unspecified affecting left dominant side
G83.33 Monoplegia, unspecified affecting right nondominant side
G83.34 Monoplegia, unspecified affecting left nondominant side
G83.4 Cauda equina syndrome
Neurogenic bladder due to cauda equina syndrome
Excludes1: cord bladder NOS (G95.8)
neurogenic bladder NOS (N31.9)
G83.5 Locked-in state
G83.8 Other specified paralytic syndromes
Excludes1: paralytic syndromes due to current spinal cord injury-code to spinal cord injury (S14, S24, S34)
G83.81 Brown-Sequard syndrome
G83.82 Anterior cord syndrome
G83.83 Posterior cord syndrome
G83.84 Todd's paralysis (postepileptic)
G83.89 Other specified paralytic syndromes
G83.9 Paralytic syndrome, unspecified

Other disorders of the nervous system (G89-G99)[edit]

G89 Pain, not elsewhere classified[edit]

Code also related psychological factors associated with pain (F45.42)
Excludes1: generalized pain NOS (R52)
pain disorders exclusively related to psychological factors (F45.41)
pain NOS (R52)
Excludes2: atypical face pain (G50.1)
headache syndromes (G44.-)
localized pain, unspecified type - code to pain by site, such as:
abdomen pain (R10.-)
back pain (M54.9)
breast pain (N64.4)
chest pain (R07.1-R07.9)
ear pain (H92.0-)
eye pain (H57.1)
headache (R51)
joint pain (M25.5-)
limb pain (M79.6-)
lumbar region pain (M54.57)
painful urination (R30.9)
pelvic and perineal pain (R10.2)
shoulder pain (M25.51-)
spine pain (M54.-)
throat pain (R07.0)
tongue pain (K14.6)
tooth pain (K08.8)
renal colic (N23)
migraines (G43.-)
myalgia (M79.1)
pain from prosthetic devices, implants, and grafts (T82.84, T83.84, T84.84, T85.84)
phantom limb syndrome with pain (G54.6)
vulvar vestibulitis (N94.810)
vulvodynia (N94.81-)
G89.0 Central pain syndrome
Déjérine-Roussy syndrome
Myelopathic pain syndrome
Thalamic pain syndrome (hyperesthetic)
G89.1 Acute pain, not elsewhere classified
G89.11 Acute pain due to trauma
G89.12 Acute post-thoracotomy pain
Post-thoracotomy pain NOS
G89.18 Other acute postprocedural pain
Postoperative pain NOS
Postprocedural pain NOS
G89.2 Chronic pain, not elsewhere classified
Excludes1: causalgia, lower limb (G57.7-)
causalgia, upper limb (G56.4-)
central pain syndrome (G89.0)
chronic pain syndrome (G89.4)
complex regional pain syndrome II, lower limb (G57.7-)
complex regional pain syndrome II, upper limb (G56.4-)
neoplasm related chronic pain (G89.3)
reflex sympathetic dystrophy (G90.5-)
G89.21 Chronic pain due to trauma
G89.22 Chronic post-thoracotomy pain
G89.28 Other chronic postprocedural pain
Other chronic postoperative pain
G89.3 Neoplasm related pain (acute) (chronic)
Cancer associated pain
Pain due to malignancy (primary) (secondary)
Tumor associated pain
G89.4 Chronic pain syndrome
Chronic pain associated with significant psychosocial dysfunction

G90 Disorders of autonomic nervous system[edit]

Excludes1: dysfunction of the autonomic nervous system due to alcohol (G31.2)
G90.0 Idiopathic peripheral autonomic neuropathy
G90.01 Carotid sinus syncope
Carotid sinus syndrome
G90.09 Other idiopathic peripheral autonomic neuropathy
Idiopathic peripheral autonomic neuropathy NOS
G90.1 Familial dysautonomia [Riley-Day]
G90.2 Horner's syndrome
Bernard(-Horner) syndrome
Cervical sympathetic dystrophy or paralysis
G90.3 Multi-system degeneration of the autonomic nervous system
Neurogenic orthostatic hypotension [Shy-Drager]
Excludes1: orthostatic hypotension NOS (I95.1)
G90.4 Autonomic dysreflexia
Use additional code to identify the cause, such as:
pressure ulcer (pressure area) (L89.-)
fecal impaction (K56.4)
urinary tract infection (N39.0)
G90.5 Complex regional pain syndrome I (CRPS I)
Reflex sympathetic dystrophy
Excludes1: causalgia of lower limb (G57.7-)
causalgia of upper limb (G56.4-)
complex regional pain syndrome II of lower limb (G57.7-)
complex regional pain syndrome II of upper limb (G56.4-)
G90.50 Complex regional pain syndrome I, unspecified
G90.51 Complex regional pain syndrome I of upper limb
G90.511 Complex regional pain syndrome I of right upper limb
G90.512 Complex regional pain syndrome I of left upper limb
G90.513 Complex regional pain syndrome I of upper limb, bilateral
G90.519 Complex regional pain syndrome I of unspecified upper limb
G90.52 Complex regional pain syndrome I of lower limb
G90.521 Complex regional pain syndrome I of right lower limb
G90.522 Complex regional pain syndrome I of left lower limb
G90.523 Complex regional pain syndrome I of lower limb, bilateral
G90.529 Complex regional pain syndrome I of unspecified lower limb
G90.59 Complex regional pain syndrome I of other specified site
G90.8 Other disorders of autonomic nervous system
G90.9 Disorder of the autonomic nervous system, unspecified

G91 Hydrocephalus[edit]

Includes acquired hydrocephalus
Excludes1: Arnold-Chiari syndrome with hydrocephalus (Q07.-)
congenital hydrocephalus (Q03.-)
spina bifida with hydrocephalus (Q05.-)
G91.0 Communicating hydrocephalus
Secondary normal pressure hydrocephalus
G91.1 Obstructive hydrocephalus
G91.2 (Idiopathic) normal pressure hydrocephalus
Normal pressure hydrocephalus NOS
G91.3 Post-traumatic hydrocephalus, unspecified
G91.4 Hydrocephalus in diseases classified elsewhere
Code first underlying condition, such as:
congenital syphilis (A50.4-)
neoplasm (C00-D48)
Excludes1: hydrocephalus due to congenital toxoplasmosis (P37.1)
G91.8 Other hydrocephalus
G91.9 Hydrocephalus, unspecified

G92 Toxic encephalopathy[edit]

Toxic encephalitis
Toxic metabolic encephalopathy
Code first (T51-T65) to identify toxic agent.

G93 Other disorders of brain[edit]

G93.0 Cerebral cysts
Arachnoid cyst
Porencephalic cyst, acquired
Excludes1: acquired periventricular cysts of newborn (P91.1)
congenital cerebral cysts (Q04.6)
G93.1 Anoxic brain damage, not elsewhere classified
Excludes1: cerebral anoxia due to anesthesia during labor and delivery (O74.3)
cerebral anoxia due to anesthesia during the puerperium (O89.2)
neonatal anoxia (P28.9)
G93.2 Benign intracranial hypertension
Excludes1: hypertensive encephalopathy (I67.4)
G93.3 Postviral fatigue syndrome
Benign myalgic encephalomyelitis
Excludes1: chronic fatigue syndrome NOS (R53.82)
G93.4 Other and unspecified encephalopathy
Excludes1: alcoholic encephalopathy (G31.2)
hypertensive encephalopathy (I67.4)
toxic (metabolic) encephalopathy (G92)
G93.40 Encephalopathy, unspecified
G93.41 Metabolic encephalopathy
Septic encephalopathy
G93.49 Other encephalopathy
Encephalopathy NEC
G93.5 Compression of brain
Arnold-Chiari type 1 compression of brain
Compression of brain (stem)
Herniation of brain (stem)
Excludes1: diffuse traumatic compression of brain (S06.2-)
focal traumatic compression of brain (S06.3-)
G93.6 Cerebral edema
Excludes1: cerebral edema due to birth injury (P11.0)
traumatic cerebral edema (S06.1-)
G93.7 Reye's syndrome
Code first (T39.0-), if salicylates-induced
G93.8 Other specified disorders of brain
G93.81 Temporal sclerosis
Hippocampal sclerosis
Mesial temporal sclerosis
G93.89 Other specified disorders of brain
Postradiation encephalopathy
G93.9 Disorder of brain, unspecified

G94 Other disorders of brain in diseases classified elsewhere[edit]

Code first underlying disease
Excludes1: encephalopathy in congenital syphilis (A50.49)
encephalopathy in influenza (J10.89)
encephalopathy in syphilis (A52.19)
hydrocephalus in diseases classified elsewhere (G91.4)

G95 Other and unspecified diseases of spinal cord[edit]

Excludes2: myelitis (G04.-)
G95.0 Syringomyelia and syringobulbia
G95.1 Vascular myelopathies
Excludes2: intraspinal phlebitis and thrombophlebitis, except non-pyogenic (G08)
G95.11 Acute infarction of spinal cord (embolic) (nonembolic)
Anoxia of spinal cord
Arterial thrombosis of spinal cord
G95.19 Other vascular myelopathies
Edema of spinal cord
Hematomyelia
Nonpyogenic intraspinal phlebitis and thrombophlebitis
Subacute necrotic myelopathy
G95.2 Other and unspecified cord compression
G95.20 Unspecified cord compression
G95.29 Other cord compression
G95.8 Other specified diseases of spinal cord
Excludes1: neurogenic bladder NOS (N31.9)
neurogenic bladder due to cauda equina syndrome (G83.4)
neuromuscular dysfunction of bladder without spinal cord lesion (N31.-)
G95.81 Conus medullaris syndrome
G95.89 Other specified diseases of spinal cord
Cord bladder NOS
Drug-induced myelopathy
Radiation-induced myelopathy
Excludes1: myelopathy NOS (G95.9)
G95.9 Disease of spinal cord, unspecified
Myelopathy NOS

G96 Other disorders of central nervous system[edit]

G96.0 Cerebrospinal fluid leak
Excludes1: cerebrospinal fluid leak from spinal puncture (G97.0)
G96.1 Disorders of meninges, not elsewhere classified
G96.11 Dural tear
Excludes1: accidental puncture or laceration of dura during a procedure (G97.41)
G96.12 Meningeal adhesions (cerebral) (spinal)
G96.19 Other disorders of meninges, not elsewhere classified
G96.8 Other specified disorders of central nervous system
G96.9 Disorder of central nervous system, unspecified

G97 Intraoperative and postprocedural complications and disorders of nervous system, not elsewhere classified[edit]

Excludes2: intraoperative and postprocedural cerebrovascular infarction (I97.81-, I97.82- )
G97.0 Cerebrospinal fluid leak from spinal puncture
G97.1 Other reaction to spinal and lumbar puncture
Headache due to lumbar puncture
G97.2 Intracranial hypotension following ventricular shunting
G97.3 Intraoperative hemorrhage and hematoma of a nervous system organ or structure complicating a procedure
Excludes1: intraoperative hemorrhage and hematoma of a nervous system organ or structure due to accidental puncture and laceration during a procedure (G97.4-)
G97.31 Intraoperative hemorrhage and hematoma of a nervous system organ or structure complicating a nervous system procedure
G97.32 Intraoperative hemorrhage and hematoma of a nervous system organ or structure complicating other procedure
G97.4 Accidental puncture and laceration of a nervous system organ or structure during a procedure
G97.41 Accidental puncture or laceration of dura during a procedure
Incidental (inadvertent) durotomy
G97.48 Accidental puncture and laceration of other nervous system organ or structure during a nervous system procedure
G97.49 Accidental puncture and laceration of other nervous system organ or structure during other procedure
G97.5 Postprocedural hemorrhage and hematoma of a nervous system organ or structure following a procedure
G97.51 Postprocedural hemorrhage and hematoma of a nervous system organ or structure following a nervous system procedure
G97.52 Postprocedural hemorrhage and hematoma of a nervous system organ or structure following other procedure
G97.8 Other intraoperative and postprocedural complications and disorders of nervous system
Use additional code to further specify disorder
G97.81 Other intraoperative complications of nervous system
G97.82 Other postprocedural complications and disorders of nervous system

G98 Other disorders of nervous system not elsewhere classified[edit]

Includes nervous system disorder NOS
G98.0 Neurogenic arthritis, not elsewhere classified
Nonsyphilitic neurogenic arthropathy NEC
Nonsyphilitic neurogenic spondylopathy NEC
Excludes1: spondylopathy (in):
syringomyelia and syringobulbia (G95.0)
tabes dorsalis (A52.11)
G98.8 Other disorders of nervous system
Nervous system disorder NOS

G99 Other disorders of nervous system in diseases classified elsewhere[edit]

G99.0 Autonomic neuropathy in diseases classified elsewhere
Code first underlying disease, such as:
amyloidosis (E85.-)
gout ( M1a-, M10.-)
hyperthyroidism (E05.-)
Excludes1: diabetic autonomic neuropathy (E09-14 with .43)
G99.2 Myelopathy in diseases classified elsewhere
Code first underlying disease, such as:
neoplasm (C00-D48)
Excludes1: myelopathy in:
intervertebral disease (M50.0-, M51.0-)
spondylosis (M47.0-, M47.1-)
G99.8 Other specified disorders of nervous system in diseases classified elsewhere
Code first underlying disorder, such as:
amyloidosis (E85.-)
avitaminosis (E56.9)
Excludes1: nervous system involvement in:
cysticercosis (B69.0)
rubella (B06.0-)
syphilis (A52.1-)