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3 Congenital bullous ichthyosiform erythroderma
- Q80.4 Harlequin fetus
- Q80.8 Other congenital ichthyosis
- Q80.9 Congenital ichthyosis, unspecified
Q81 Epidermolysis bullosa
- Q81.0 Epidermolysis bullosa simplex
- Excludes1: Cockayne's syndrome (Q87.1)
- Q81.1 Epidermolysis bullosa letalis
- Herlitz' syndrome
- Q81.2 Epidermolysis bullosa dystrophica
- Q81.8 Other epidermolysis bullosa
- Q81.9 Epidermolysis bullosa, unspecified
Q82 Other congenital malformations of skin
- Excludes1: acrodermatitis enteropathica (E83.2)
- congenital erythropoietic porphyria (E80.0)
- pilonidal cyst or sinus (L05.-)
- Sturge-Weber (-Dimitri) syndrome (Q85.8)
- Q82.0 Hereditary lymphedema
- Q82.1 Xeroderma pigmentosum
- Q82.2 Mastocytosis
- Urticaria pigmentosa
- Excludes1: malignant mastocytosis (C96.2)
- Q82.3 Incontinentia pigmenti
- Q82.4 Ectodermal dysplasia (anhidrotic)
- Excludes1: Ellis-van Creveld syndrome (Q77.6)
- Q82.5 Congenital non-neoplastic nevus
- Birthmark NOS
- Flammeus Nevus
- Portwine Nevus
- Sanguineous Nevus
- Strawberry Nevus
- Vascular Nevus NOS
- Verrucous Nevus
- Excludes2: caf? au lait spots (L81.3)
- lentigo (L81.4)
- nevus NOS (D22.-)
- araneus nevus (I78.1)
- melanocytic nevus (D22.-)
- pigmented nevus (D22.-)
- spider nevus (I78.1)
- stellar nevus (I78.1)
- Q82.8 Other specified congenital malformations of skin
- Abnormal palmar creases
- Accessory skin tags
- Benign familial pemphigus [Hailey-Hailey]
- Congenital