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type IVB

E76.219 Morquio mucopolysaccharidoses, unspecified

Morquio syndrome

Mucopolysaccharidosis, type IV

E76.22 Sanfilippo mucopolysaccharidoses

Mucopolysaccharidosis, type III (A) (B) (C) (D)

Sanfilippo A syndrome

Sanfilippo B syndrome

Sanfilippo C syndrome

Sanfilippo D syndrome

E76.29 Other mucopolysaccharidoses

beta-Glucuronidase deficiency

Maroteaux-Lamy (mild) (severe) syndrome

Mucopolysaccharidosis, types VI, VII

E76.3 Mucopolysaccharidosis, unspecified

E76.8 Other disorders of glucosaminoglycan metabolism

E76.9 Glucosaminoglycan metabolism disorder, unspecified

E77 Disorders of glycoprotein metabolism

E77.0 Defects in post-translational modification of lysosomal enzymes

Mucolipidosis II [I-cell disease]

Mucolipidosis III [pseudo-Hurler polydystrophy]

E77.1 Defects in glycoprotein degradation

Aspartylglucosaminuria

Fucosidosis

Mannosidosis

Sialidosis [mucolipidosis I]

E77.8 Other disorders of glycoprotein metabolism

E77.9 Disorder of glycoprotein metabolism, unspecified

E78 Disorders of lipoprotein metabolism and other lipidemias

Excludes1: sphingolipidosis (E75.0-E75.3)

E78.0 Pure hypercholesterolemia

Familial hypercholesterolemia

Fredrickson's hyperlipoproteinemia, type IIa

Hyperbetalipoproteinemia

Hyperlipidemia, Group A

Low-density-lipoprotein-type [LDL] hyperlipoproteinemia

E78.1 Pure hyperglyceridemia

Elevated fasting triglycerides

Endogenous hyperglyceridemia

Fredrickson's hyperlipoproteinemia, type IV

Hyperlipidemia, group B

Hyperprebetalipoproteinemia

Very-low-density-lipoprotein-type [VLDL] hyperlipoproteinemia

E78.