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- Use additional code to identify:
- dementia with behavioral disturbance (F02.81)
- dementia without behavioral disturbance (F02.80)
- A81.0 Creutzfeldt-Jakob disease
- A81.00 Creutzfeldt-Jakob disease, unspecified
- Jakob-Creutzfeldt disease, unspecified
- A81.01 Variant Creutzfeldt-Jakob disease
- vCJD
- A81.09 Other Creutzfeldt-Jakob disease
- CJD
- Familial Creutzfeldt-Jakob disease
- Iatrogenic Creutzfeldt-Jakob disease
- Sporadic Creutzfeldt-Jakob disease
- Subacute spongiform encephalopathy (with dementia)
- A81.00 Creutzfeldt-Jakob disease, unspecified
- A81.1 Subacute sclerosing panencephalitis
- Dawson's inclusion body encephalitis
- Van Bogaert's sclerosing leukoencephalopathy
- A81.2 Progressive multifocal leukoencephalopathy
- Multifocal leukoencephalopathy NOS
- A81.8 Other atypical virus infections of central nervous system
- A81.81 Kuru
- A81.82 Gerstmann-Sträussler-Scheinker syndrome
- GSS syndrome
- A81.83 Fatal familial insomnia
- FFI
- A81.89 Other atypical virus infections of central nervous system
- A81.9 Atypical virus infection of central nervous system, unspecified
- Prion diseases of the central nervous system NOS
A82 Rabies
- A82.0 Sylvatic rabies
- A82.1 Urban rabies
- A82.9 Rabies, unspecified
A83 Mosquito-borne viral encephalitis
- Includes: mosquito-borne viral meningoencephalitis
- Excludes2: Venezuelan equine encephalitis (A92.2)
- West Nile fever (A92.3-)
- West Nile virus (A92.3-)
- A83.0 Japanese encephalitis
- A83.1 Western equine encephalitis
- A83.2 Eastern equine encephalitis
- A83.3 St Louis encephalitis
- A83.4 Australian encephalitis
- Kunjin virus disease
- A83.5 California encephalitis
- California meningoencephalitis